Subacute late-onset cerebellar ataxia in a patient can be due to varied causes. The common ones are infectious, drug-related, autoimmune and paraneoplastic pathologies. As majority of these causes are deemed treatable, they should be investigated in a sporadic case of ataxia. Celiac disease can have neurological complications in about 10% of cases but those are usually a secondary feature of this disease. This case report features a case of rapidly progressive cerebellar ataxia as the sole presentation of unsuspected celiac disease.